To report a case of low-grade adenocarcinoma of the retinal pigment epithelium (RPE) in a young Asian woman.
Methods
Interventional case report with histopathologic correlation.
Results
A 28-year-old Asian woman with a year-long history of floaters presented with a dark pigmented lesion in the right eye. Partial lamellar sclerouvectomy was performed and histopathology revealed a retina pigment epithelial neoplasm consistent with a low-grade adenocarcinoma. The patient responded well to the surgery with no complications.
Conclusions
Neoplasms of RPE are rare but must be differentiated from choroidal melanoma, as they do not tend to metastasize. Local resection can be a good option for peripheral RPE tumors.
ShieldsJ.A., ShieldsC.L.Tumors and related lesions of the pigment epithelium. In: Intraocular Tumors: An Atlas and Text Book.Philadelphia: Lippincott Williams & Wilkins, 2008; 432–79.
2.
ShieldsJ.A., ShieldsC.L., GündüzK., EagleR.C.Jr.. Neoplasms of the retinal pigment epithelium. The 1998 Albert Ruedemann, Sr, Memorial lecture, Part 2. Arch Ophthalmol1999; 117: 601–8.
3.
ShieldsJ.A., ShieldsC.L., GündüzK., EagleR.C.Jr.. Adenoma of the ciliary body pigment epithelium: the 1998 Albert Ruedemann, Sr, Memorial Lecture, Part 1. Arch Ophthalmol1999; 117: 592–7.
4.
JampelH.D., SchachatA.P., ConwayB.Retinal pigment epithelial hyperplasia assuming tumor-like proportions. Report of two cases. Retina1986; 6: 105–12.
5.
ShieldsJ.A., ShieldsC.L., SlakterJ., WoodW., YannuzziL.A.Locally invasive tumors arising from hyperplasia of the retinal pigment epithelium. Retina2001; 21: 487–92.
6.
ShieldsJ.A., ShieldsC.L., EagleR.C.Jr., SinghA.D.Adenocarcinoma arising from congenital hypertrophy of the retinal pigment epithelium. Arch Ophthalmol2001; 119: 597–602.
