Pigmented dermatofibrosarcoma protuberans (Bednar tumor) is a rare neoplasm accounting for approximately 1–5% of all cases of dermatofibrosarcoma protuberans. The majority occurs on the trunk, and the remainders are more or less equally distributed in the upper and lower extremities and the head and neck. Microscopically it is characterized by spindled cells arranged in a tight storiform pattern and admixed with a small population of melanin-containing dendritic cells. The dendritic cells are the primary feature that distinguish this lesion from conventional dermatofibrosarcoma protuberans.
We report here a case of Bednar tumor occurring on the dorsal aspect of the foot in a young female.
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References
1.
. AkasakaT.OhyamaN.KonS.A case of pigmented dermatofibrosarcoma protuberans (Bednar tumor)J Dermatol.24: 390–394, 1997.
2.
. BednarB.Stroriform neurofibromas of the skin, pigmented and nonpigmented. Cancer10: 368–376, 1957.
3.
. DingJ.HashimotoH.SugimotoT.TsuneyoshiM.EnjojiM.Bednar tumor (pigmented dermatofibrosarcoma protuberans): an analysis of six cases. Acta Pathol Jpn.40: 744–754, 1990.
. ElgartG.W.HanlyA.BussoM.SpencerJ.M.Bednar tumor (pigmented dermatofibrosarcoma protuberans) occurring in a site of previous immunization: immunochemical findings and therapy. J. Am. Acad. Dermatol.40: 315–317, 1999.
6.
. KaburagiY.HattaN.KawaraS.TakeharaK.Pigmented dermatofibrosarcoma protuberans (Bednar tumor) occurring in a Japanese infant. Dermatol.197: 48–51, 1998.
. MarcuJ.R.FewJ.W.SengerC.ReynoldsM.Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population. J. Pediatr. Surg.33: 1811–1814, 1998.
9.
. MochizukiY.NarisawaY.KohdaH.A case of Bednar tumor recurring after 23 years. J. Dermatol.23: 614–618, 1996.
10.
. OnodaN.TsutsumiY.KakudoK.OzawaA.NiizumaK.OhkidoM.OsamuraR.Y.Pigmented dermatofibrosarcoma protuberans (Bednar tumor): An autopsy case with systemic metastasis. Acta Pathol Jpn.40: 935–940, 1990.
