The pathogenesis and therapy of shrinking lungs syndrome in patients with systemic lupus erythematosus remains controversial. It has been previously reported that corticosteroid treatment can be effective. We report a patient with shrinking lungs syndrome who presented a good response to inhaled beta-agonist therapy. Therapeutic approach to this syndrome is discussed.
Orens JB, Martinez FJ, Lynch III JP. Pleuropulmonary manifestations of systemic lupus erythematosus . Rheum Dis Clin North Am1994; 20: 159-193.
2.
Andonopoulos AP et al. Pulmonary function of nonsmoking patients with systemic lupus erythematosus. Chest1988 ; 94: 312—315.
3.
Jacobelli S. et al. Inspiratory muscle dysfunction and unexplained dyspnea in systemic lupus erythematosus. Arthritis Rheum1985; 28: 781-788.
4.
Laroche CM et al. Diaphragm strength in the shrinking lungs syndrome of systemic lupus erythematosus. Q J Med1989; 71: 429-439.
5.
Stevens Wmr, Clemens LE, Burdon Jgw, Webb J.The 'shrinking lungs syndrome'. An infrequently recognised feature of systemic lupus erythematosus. Aust NZ J Med1990; 20: 67-70.
