Chemie Und Biochemie Des Cystins Und Cysteins

Ackermann P. G. , Kheim T. : Clin. Chem., 10; 32 (1964).

Ames G. F. : Uptake of amino acids by Salmonella typhimurium. Arch. Biochem. Biophys., 104; 1–18 (1964).

Anslow W. P. jr. , Simmonds S. , du Vigneaud V. : The synthesis of the isomers of cystathionine and a study of their availability in sulfur metabolism. J. Biol. Chem., 166; 35 (1946).

Arrow U. K. , Westall R. G. : Amino acid clearances in cystinuria. J. Physiol., 142; 141–146 (1953).

Asafoor A. M. , Lacey B. W. , London D. R. , Milne M. D. : Amino acid metabolism in cystinuria. Clin. Sci., 23; 285–304 (1962).

Becker F. F. , Green H. : Incorporation of cystine and lysine by normal and « cystinuric » leucocytes. Proc. Soc. Exp. Biol., 99; 694–696 (1958).

Black S. : The biochemistry of sulfur containing compounds. Ann. Res. Biochem., 32; 399 (1963).

Brand E. , Block R. J. , Kassell B. , Cahill G. F. : Carboxymethylcystine metabolism, its implications on therapy in cystinuria and on methionine-cysteine relationship. Proc. Soc. Exp. Biol. Med., 35; 501 (1936).

Brand E. , Cahill G. F. , Block R. J. : Cystinuria. IV. The metabolism of homocysteine and homocystine. J. Biol. Chem., 110; 399 (1935).

Brand E. , Harris M. M. , Biloon S. : J. Biol. Chem., 86; 315 (1930).

Cafruny E. J. , Carhoart E. , Farah A. : Effects of hypophysectomy and hormones on sulfhydryl concentrations in rat kidney cells. Endocrinology, 61; 143 (1957).

Christensen H. N. : Elektrolytstoffwechsel. Springer-Verlag, Berlin-Heidelberg-New York 1969, S. 83.

Clayton B. E. , Patrick A. D. : Use of dimercaptol or penicillamine in the treatment of cystinosis. Lancet. 2; 909 (1961).

Crawhall J. C. , Scowen E. F. , Watts R. W. E. : Effect of penicillamine on cystinuria. Brit. Med. J., 1; 588 (1963).

Curnow D. H. , Lynch W. J. : Amer. J. Clin. Pathol., 51; 547 (1969).

Dent C. E. , Senior B. : Brit. J. Urol., 27; 317–332 (1955).

Dent C. E. , Rose G. A. : Amino acid metabolism in cystinuria. Quart. J. Med., 20; 205–219 (1951).

Dent C. E. , Senior B. , Walshe J. M. : The pathogenesis of cystinuria. II. Polarographic studies of the metabolism of sulphur-containing amino acids. J. Clin. Invest., 33; 1216–1226 (1954).

Dent C. E. , Senior B. : Studies on the treatment of cystinuria. Brit. J. Urol., 27; 317–332 (1955).

Dickinson J. C. , Rosenblum H. , Hamilton P. B. : Pediatrics, 36; 2 (1965).

Eagle H. , Piez K. A. , Oyama V. I. : The biosynthesis of cystine in human all cell cultures. J. Biol. Chem., 236; 1425 (1961).

Edsall J. T. : Advances in Protein Chemistry, 3; 415 (1947).

Evered D. F. : Biochem. J., 62; 416 (1956).

Fernandez A. A. , Henry R. J. : Anal. Biochem., 11; 190 (1965).

Gardner J. D. , Levy A. G. : Transport of dibasic amino acids by human erythrocytes. Metabolism, 21; 413–431 (1972).

Goldman H. , Scriver C. R. , Aaron K. , Pinsky L. : Use of dithiothreitol to correct cystine storage in cultured cystinotic fibroblasts. Lancet, 1; 811 (1970).

Gross J. B. , Comfort M. W. , Ulrich J. A. : Abnormalities in serum and urinary amino acids in hereditary and non-hereditary pancreatitis. Trans. Ass. Amer. Phys., 70; 127–139 (1957).

Gross J. B. , Ulrich J. A. , Jones J. D. , Maker F. T. : Endogenous renal clearances of 12 individual amino acids in four apparently healthy subjects and in four aminoaciduric person of a kindred with hereditary pancreatitis. J. Lab. Clin. Med., 63; 933–944 (1964).

Groth U. , Rosenberg L. E. : Transport of dibasic amino acids, cystine, and tryptophan by cultured human fibroblasts: Absence of a defect in cystinuria and Hartnup disease. J. Clin. Invest., 51; 2130–2142 (1972).

Seegmiller P. , Natelson S. : Clin. Chem., 16; 366 (1970).

Henry R. J. , Cannon D. C. , Winkelman J. W. : Clinical chemistry Principles and Technics. Harper & Row Publ., New York-London 1974, p. 592.

Kallistratos G. : Die Bedeutung des Aussalzeffektes für die Harnsteinentstehung - prophylaxe und - therapie, in: Pathogenese und Klinik der Harnsteine II (Hsg. Vahlensieck und G. Gasser), Bd. 4 der Reihe Fortschritte der Urologie und Nephrologie (Hsg. W. Vahlensieck) Dr. D. Steinkopff-Verlag, Darmstadt (1974), S. 56-80.

Kennedy G. C. , Lewin D. C. , Lunn H. F. : Guy's Hosp. Rept., 88; 34 (1938).

Kolb F. O. , Earl J. M. , Harper H. A. : Disappearance of cystinuria in a patient treated with prolonged low methionine dict. Metabolism, 16; 378–381 (1967).

MacDonald W. B. , Fellers F. X. : Amer. J. Clin. Pathol., 49; 123 (1968).

Mazia D. : The Role of Thiol Groups in the Structure and Function of the Mitotic Apparatus. In: Sulfur in Proteins ( Benesch R. , Klotz I. M. , Middlebrook W. R. , Boyer P. D. , Szent Gyorgi A. G. , and Schwarz D. R. , eds). Academic Press, New York 1959, p. 367.

McMeekin T. L. , Cohn E. J. , Blanchard M. H. : J. Amer. chem. Soc., 59; 2717 (1939).

Medes G. : Biochem. J., 31; 12 (1939).

Middleton J. E. : J. Clin. Pathol., 23; 90 (1970).

Milne M. D. , Asatoor A. M. , Edwards K. D. G. , Loughridge L. W. : The intestinal absorption defect in cystinuria. Gut, 2; 323–337 (1961).

Mize C. E. , Thompson T. E. , Langdon R. G. : Hepatic glutathione reductase: II. Physical properties and mechanism of action. J. Biol. Chem., 237; 1956 (1962).

Mize C. E. , Langdon R. G. : Hepatic glutathione reductase: I. Purification and general kinetic properties. J. Biol. Chem., 237; 1589 (1962).

Perry R. L. , Hansen S. : Clin. Chem. Acta, 25; 53 (1969).

Perry T. L. , Hansen S. , Diamond S. , Stedman D. : Lancet, 1; 806 (1969).

Reed L. J. , Cavallini D. , Plum F. , Rachele J. R. , du Vigneaud V. : The conversion of methionine to cystine in a human cystinurie. J. Biol. Chem., 180; 783 (1949).

Remien A. , Kallistratos G. , Burchardt P. : Die Behandlung der Cystinsteinerkrankung mit Alpha-Mercapto-Propionylglycin, in: Pathogenese und Klinik der Harnsteine IV (W. Vahlensieck und G. Gasser, Hsg.), Dr. D. Steinkopff-Verlag, Darmstadt 1975, S. 198.

Remien A. , Kallistratos G. , Burchardt P. : Treatment of cystinuria with Thiola (Alpha-Mercaptopropionyl Glycine), Eur. Urol., 1; 227–228 (1975).

Robson E. B. , Rose G. A. : The effect of intravenous lysine on the renal clearances of cystine, arginine and ornithine in normal subjects, in patients with cystinuria and Fanconi syndroms and in their relatives. Clin. Sci., 16; 75–91 (1957).

Rootwelt K. : Scand. J. Clin. Lab. Invest., 19; 325 (1967).

Rosenberg L. E. , Downing S. J. : Transport of neutral and dibasic amino acids by human leucocytes: Absence of defect in cystinuria. J. Clin. Invest., 44; 1382–1393 (1965).

Rosenthal A. F. , Yaseen A. : Clin. Chim. Acta, 26; 363 (1969).

Sano K. : Solubility of amino acids with changes of pH. Biochem. Z., 168; 14 (1926).

Schneider J. A. , Bradley K. , Seegmiller J. E. : Increased cystine in leucocytes from individuals homozygous and heterozygous for cystinosis. Science, 157; 1321 (1967).

Schneider J. A. , Rosenbloom F. M. , Bradley K. H. , Seegmiller J. E. : Increased free cystine content of fibroblasts cultured from patients with cystinosis. Biochem. Biophys. Res. Commun., 29; 527–531 (1967).

Schneider J. A. , Bradley K. , Seegmiller J. E. : Increased cystine in leucocytes from individuals homozygous and heterozygous for cystinosis. Science, 157; 1321–1322 (1967).

Schneider J. A. , Bradley K. H. , Seegmiller J. E. : Transport and intracellular fate of cysteine- ³⁵S in leucocytes from normal subjects and patients with cystinosis. Pediat. Res., 2; 441–450 (1968).

Seegmiller J. E. , Friedmann T. , Harrison H. E. , Wong V. , Schneider J. A. : Cystinosis. Ann. intern. Med., 68; 883 (1968).

Shinohara K. , Padis L. E. : J. Biol. Chem., 112; 709 (1935).

Shinohara K. , Padis L. E. : J. Biol. Chem., 112; 709 (1935).

Smith D. R. , Kolb F. O. , Harper H. A. : Management of cystinuria and cystine-stone disease, J. Urol., 81; 61 (1959).

Smith D. R. , Kolb F. O. , Harper H. A. : Management of cystinuria and cystine-stone disease. J. Urol., 81; 61–69 (1959).

Stetten De W. jr. : The fate of dietary serine in the body of the rat. J. Biol. Chem., 144; 501 (1942).

Sullivan M. X. , Hess W. C. : J. Biol. Chem., 116; 221 (1936).

Thier S. , Fox M. , Segal S. , Rosenberg L. E. : Cystinuria: in vitro demonstration of an intestinal transport defect. Science, 143; 432–484 (1964).

Tietze F. : Disulfide reduction in rat liver. II. Chromatographic separation of nucleotide-dependent disulfide reductase and GSH-disulfide transhydrogenase activities of the high-speed supernatant fraction. Biochem. Biophys. Acta, 220; 449 (1970).

Tietze F. : Disulfide reduction in rat liver. I. Evidence for the presence of nonspecific nucleotide-dependent disulfide reductase and GSH-disulfide transhydrogenase activities in the high-speed supernatant fraction. Arch. Biochem. Biophys., 138; 177 (1970).

Timmermann A. , Kallistratos G. , Fenner O. , Sommer E. : A tentative wap suggesting the possible role of urinary minerals for the formation of renal stones, in: Proceedings of the renal stone research symposium, held at Leeds April, 1968 ( Hodgkinson A. and Nordin B.E.C. , eds.), J. A. Churchill Ltd., London 1969, p. 273–288.

Uhlendorf P. W. , Mudd S. H. : Cystathionine synthase in tissue culture derived from human skin. Enzyme defect in homocystinuria. Science, 160; 1007 (1968).

Virtue R. W. , Lewis H. B. : J. Biol. Chem., 140; 415 (1934).

Worthen H. G. , Good R. A. : The pathogenesis of cystinosis. Amer. J. Dis. Child., 102; 494 (1961).

Wroblewski F. : Pure Appl. Chem., 3; 385 (1961).

Zinneman H. H. , Jones J. E. : Dietary methionine and its influence on cystine excretion in cystinuric patients. Metabolism, 15; 915–921 (1966).