Radiographic Features of Lobar Agenesis of the Liver

Abstract

Purpose:

Our aim was to describe the radiographic features of lobar agenesis of the liver.

Material and Methods:

Six patients with lobar agenesis of the liver, 5 right- and one left-sided, are presented. CT was used to confirm diagnosis. Chest radiography, barium meals, and urograms were also analyzed.

Results:

In right-sided agenesis, the following were observed: a) hammock or U-shaped deformity of the stomach; b) colonic interposition of the diaphragm (Chilaiditi's syndrome); and c) reversal of the cranial orientation of the colonic hepatic flexure compared to the splenic flexure. The right kidney was higher in position than the left in both right- and left-sided lobar agenesis.

Conclusion:

Our radiographic findings can provide a multidisciplinary approach in the identification of this anatomic anomaly.

Keywords

Liver stomach congenital anomaly CT

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