A 50-year-old man with a primary tricuspid valve intimal sarcoma and right ventricular and pulmonary arterial tumors with metastases to the chest wall and lung, confirmed on plain radiographs initially, presented with a cough. He underwent palliative complete removal of the cardiac tumor and partial removal of the right pulmonary arterial tumor with tricuspid valve replacement, to avoid sudden death caused by tumor embolization and to definitively diagnose the cardiac tumor. The cardiac tumor arose from the tricuspid valve leaflets. Nine months postoperatively, the patient died secondary to fatal progression of the pulmonary arterial and lung tumors.
BurkeATavoraF.The 2015 WHO classification of tumors of the heart and pericardium.J Thorac Oncol2016;
11: 441–52.
2.
ShahDKJoyceLDGroganM, et al.
Recurrent pulmonary intimal sarcoma involving the right ventricular outflow tract.Ann Thorac Surg2011;
91: e41–2.
3.
NeuvilleACollinFBrunevalP, et al.
Intimal sarcoma is the most frequent primary cardiac sarcoma: clinicopathologic and molecular retrospective analysis of 100 primary cardiac sarcomas.Am J Surg Pathol2014;
38: 461–9.
4.
RamlawiBLejaMJAbu SalehWK, et al.
Surgical treatment of primary cardiac sarcomas: review of a single-institution experience.Ann Thorac Surg2016;
101: 698–702.
