Intrapulmonary artery septation is employed in patients with unbalanced pulmonary artery growth. A baby girl received a systemic pulmonary shunt in the neonatal period and bilateral Glenn shunts in early infancy. Once the Glenn shunts were established, the right pulmonary artery became hypoplastic. We performed intrapulmonary artery septation involving the Glenn shunts to the left pulmonary artery and the systemic pulmonary shunt to the right pulmonary artery. As early as 3 months after intrapulmonary artery septation, right pulmonary artery growth was observed. Eventually, Fontan circulation was achieved with fenestration.
BachaEALangPMayerJEJrMcElhinneyDB. Connection of discontinuous pulmonary arteries in patients with a superior or total cavopulmonary circulation. Ann Thorac Surg2008; 86: 1948–1954.
3.
SakamotoKIkaiAFujimotoYOtaN. Novel surgical approach ‘intrapulmonary-artery septation’ for Fontan candidates with unilateral pulmonary arterial hypoplasia or pulmonary venous obstruction. Interact Cardiovasc Thorac Surg2007; 6: 150–154.
4.
TachiMMurataMIdeYItoHKannoKImaiKSakamotoK. Efficacy of the ‘intrapulmonary-artery septation’ surgical approach for Fontan candidates with unilateral pulmonary arterial hypoplasia. Eur J Cardiothorac Surg2016; 49: 183–187.
5.
ChowdhuryUKAiranBSharmaRet al.Univentricular repair in children under 2 years of age: early and midterm results. Heart Lung Circ2001; 10: 3–13.
