We present the case of a 2-year-old girl with congenital stenosis of the left inferior pulmonary vein associated with a large perimembranous ventricular septal defect. The child underwent repair of the left inferior pulmonary vein with autologous left atrial appendage as a pedicled tube, followed by closure of the ventricular septal defect. Important technical steps to minimize the restenosis rate are highlighted.
EdwardsJE. Congenital stenosis of pulmonary veins. Pathologic and developmental considerations. Lab Invest1960; 9: 46–66.
2.
KawashimaYUedaTNaitoYMorikawaEManabeH. Stenosis of pulmonary veins: report of a patient corrected surgically. Ann Thorac Surg1971; 12: 196–202.
3.
DevaneyEJChangACOhyeRGBoveEL. Management of congenital and acquired pulmonary vein stenosis. Ann Thorac Surg2006; 81: 992–995.
4.
LiuYLShenXDLiJR. Repair of congenital pulmonary vein stenosis. World J Pediatr2006; 4: 308–310. Available at: http://wjpch.com/UploadFile/0604011.pdf. Accessed May 12, 2018.
5.
YunTJColesJGKonstantinovIEet al.Conventional and sutureless techniques for management of the pulmonary veins: evolution of indications from postrepair pulmonary vein stenosis to primary pulmonary vein anomalies. J Thorac Cardiovasc Surg2005; 129: 167–174.
6.
PacificoADMandkeNVMcGrathLBColvinEVBiniRMBargeronLMJr. Repair of congenital pulmonary venous stenosis with living autologous atrial tissue. J Thorac Cardiovasc Surg1985; 89: 604–609.
7.
MendelsohnAMBoveELLupinettiFMet al.Intraoperative and percutaneous stenting of congenital pulmonary artery and vein stenosis. Circulation1993; 88(Suppl II): II210–II217.
8.
MendeloffENSprayTLHuddlestonCBBridgesNDCanterCBMalloryGBJr. Lung transplantation for congenital pulmonary vein stenosis. Ann Thorac Surg1995; 60: 903–906.
