The majority of patients with double-chambered right ventricle present during childhood; it is rarely treated in adults. We report the case of a 71-year-old woman who presented with mild fatigue for 2 years. Investigation of an ejection systolic murmur revealed a double-chambered right ventricle with a peak gradient of 147 mm Hg across the right ventricular outflow tract. Substantial right ventricular muscle bundle resection and augmentation of the right ventricular outflow tract with a bovine pericardial patch were performed after a right ventriculotomy.
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