We describe an extremely rare form of double-outlet right ventricle in a 1-year-old boy who had 1-malposition of the great arteries with the definitive conotruncal features of false Taussig-Bing heart. Extraordinary conotruncal morphology raised several surgical options, however, the definitive anatomical repair was achieved by an arterial switch operation with a baffle from a ventricular septal defect to the pulmonary artery.
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Van PraaghRPérez-TrevinoCReynoldsJLMoesCAKeithJDRoyDLDouble outlet right ventricle (S,D,L) with subaortic ventricular septal defect and pulmonary stenosis. Report of six cases. Am J Cardiol1975;35:42–53.
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KurosawaHVan MieropLH. Surgical anatomy of the infundibular septum in transposition of the great arteries with ventricular septal defect. J Thorac Cardiovasc Surg1986;91:123–32.
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MoritaKKurosawaHKoyanagiKNomuraKUnoYNaganumaHAtrioventricular groove patch plasty for anatomically corrected malposition of the great arteries. J Thorac Cardiovasc Surg2001;122:872–8.
