Congenital cystic adenomatoid malformation is rare in adults, and often asymptomatic. We describe a case of malignant degeneration of a congenital cystic adenomatoid malformation in a 77-year-old man. Congenital cystic adenomatoid malformation must be considered a premalignant lesion, even in older patients. Rigorous preoperative staging must be undertaken. Anatomic resection with extensive lymphadenectomy remains the treatment of choice.
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BeasleyMBBrambillaETravisWD. The 2004 World Health Organization classification of lung tumors [Review]. Semin Roentgenol2005;40:90–7.
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LantuejoulSFerrettiGRGoldstrawPHansellDMBrambillaENicholsonAG. Metastases from bronchioloalveolar carcinomas associated with long-standing type 1 congenital cystic adenomatoid malformations. A report of two cases. Histopathology2006;48:204–6.
