A 19-year-old girl with bicuspid aortic valve and Turner-like stigmata underwent a successful repair with a cusp extension technique using fresh autologous pericardium for aortic insufficiency. She also had a simultaneous artificial graft replacement for ascending aortic dilatation. Aortic valve function showed no significant stenosis and slight insufficiency 2 years postoperatively. This technique is recommended to avoid a Ross or Ross/Konno procedure because of its ready availability, simplicity and excellent midterm results.
Get full access to this article
View all access options for this article.
References
1.
DuranCMGometzaBKumarNGalloRBjornstadK. From aortic cusp extension to valve replacement with stentless pericardium. Ann Thorac Surg1995; 60 (2 Sppl): S428–32.
2.
KalangosABeghettiMBaldovinosAValaDBichelTMermillodB. Aortic valve repair by cusp extension with the use of fresh autologous pericardium in children with rheumatic aortic insufficiency. J Thorac Cardiovasc Surg1999; 118: 225–36.
3.
LinAELippeBRosenfeldRG. Further delineation of aortic dilation, dissection, and rupture in patients with Turner syndrome. Pediatrics1998; 102: e12.
4.
LinAELippeBMGeffnerMEGomesALoisJFPartonCW. Aortic dilation, dissection, and rupture in patients with Turner syndrome. J Pediatr1986; 109: 820–6.
5.
AllenDBHendricksSALevyJM. Aortic dilation in Turner syndrome. J Pediatr1986; 109: 302–5.
6.
HahnRTRomanMJMogtaderAHDevereuxRB. Association of aortic dilation with regurgitant, stenotic and functionally normal bicuspid aortic valves. J Am Coll Cardiol1992; 19: 283–8.
7.
McDonaldGRSchaffHVPyeritzREMcKusickVAGottVL. Surgical management of patients with the Marfan syndrome and dilatation of the ascending aorta. J Thorac Cardiovasc Surg1981; 81: 180–6.
8.
RomanMJDevereuxRBKramer-FoxRO'LoughbinJ. Two-dimensional echocardiographic aortic root dimensions in normal children and adults. Am J Cardiol1989; 64: 507–12.
