A case of unilateral complete aplasia of the petrous apex and inner ear associated with retype tracheoesophageal fistula is reported. Polytomography, computerized axial tomography, and plain film radiography confirmed the presence of this rare variant of inner ear aplasia. This patient, who has normal facial nerve function, is, to our knowledge, the first reported case of a nonthalidomide, Michel-type aplasia since the original report of Michel more than a century ago. Unilateral complete inner ear aplasia associated with tracheoesophageal fistula has not been previously reported.
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References
1.
MichelEM: Memoire sur les anomalies congenitales de l'oreille intern. Gaz Med Strasb3: 55–58, 1863.
2.
ValvassoriGENauntonRFLindsayJR: Inner ear anomalies: Clinical and histopathological considerations. Ann Otol78: 929–938, 1969.
3.
JorgensenMD: Thalidomide induced aplasia of the inner ear. J Laryngol78: 1095–1101, 1964.
4.
BalinskyBI: An Introduction to Embryology, ed 4. Philadelphia, WB Saunders Co, 1975, pp 367–370.
5.
LewisWH: On the origin and differentiation of the otic vesicle in amphibian embryos. Anat Rec1: 141–145, 1907.
6.
MyersENStoolSWeltschewA: Congenital anomaly of the middle and inner ear. Laryngoscope8: 344–351, 1968.
7.
AltmannF: The inner ear in genetically determined deafness. Acta Otolaryngol, suppl 187, 1964, p 39.
