Abstract
Objective: Pediatric patients with neurofibromatosis type 2 (NF2) present a unique and difficult challenge to the neurotologist. The participants should be able to discuss the various approaches to pediatric patients with NF2 in regard to hearing preservation techniques and individualized management strategies.
Method: Case study format. Five unique clinical scenarios demonstrate various surgical approaches and management techniques for hearing preservation.
Results: Patients with NF2 are still developing physically, mentally, and socially. They generally have a poorer prognosis and diminished life expectancy compared to adult patients. Considerations of utmost importance include management of the tumor with the goal of minimizing outcomes such as significant bilateral hearing loss, facial paralysis, and injury to other cranial nerves. This review provides insight into clinical challenges associated with NF2 and illuminates the therapeutic options for hearing preservation and optimized quality of life in these patients. Each case clearly demonstrates important management principles that provide a framework for care of the pediatric NF2 patient.
Conclusion: Each patient with NF2 is unique. Methods to preserve hearing must be individually tailored in order to preserve optimal hearing and avoid disruption of the development of the pediatric patient.
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