ElbornJS, ShaleDJ, BrittonJR. Cystic fibrosis: current survival and population estimates to the year 2000.Thorax1991; 46: 881–5.
2.
Scott-JuppR, LamaM, TannerMS. Prevalence of liver disease in cystic fibrosis.Arch Dis Child1991; 66: 698–701.
3.
OppenheimerEH, EsterlyJR. Hepatic changes in young infants with cystic fibrosis: possible relation to focal biliary cirrhosis.J Pediatr1975; 86: 683–9.
4.
RoyCC, WebbedAM, MorinCLHepatobiliary disease in cystic fibrosis: a survey of current issues and concepts.J Pediatr Gastroenterol Nutr1992; 1: 469–78.
5.
CohnJA, StrongTV, PiccoloMR, CairnAC, ColleensFS, FitDIG. Localization of the cystic fibrosis transmembrane conductance regulator in human bile duct epithelial cells.Gastroenterology1993; 106: 1857–64.
6.
TannerMS. Liver and biliary problems in cystic fibrosis.J R Soc Med1992; 85(Suppl. 19): 20–4.
ColomboC, ApostoloMG, FerrariMAnalysis of risk factors for the development of liver disease associated with cystic fibrosis.J Pediatr1994; 124: 393–9.
9.
Noble-JamiesonG, ValenteJ, BarnesNDLiver transplantation for hepatic cirrhosis in cystic fibrosis.Arch Dis Child1994; 71: 349–52.
10.
TannerMS. Liver disease in cystic fibrosis.Arch Dis Child1995; 72: 281–4.
11.
CarryH.Abdominal radiology in cystic fibrosis.J R Soc Med1995; 88(Suppl. 25): 18–23.
12.
O'ConnorPJ, SouthernKW, BowlerIM, IrvingHC, RobinsonPJ, LittlewoodJM. The role of hepatobiliary scintigraphy in cystic fibrosis.Hepatology1996; 23: 281–7.
13.
ErlingerS, DumontM.Influence of ursodeoxycholic acid on bile secretion. In: PaumgartnerG, StiehlA, BarbaraL, eds. Strategies for the treatment of hepatobiliary disease.Dordrecht: Kluwer Academic, 1990;pp. 35–42.
14.
PouponRE, PouponR, BalkauB, and the UDCA-PBC study group. Ursodiol for the long-term treatment of primary biliary cirrhosis.N Engl J Med1994; 330: 1342–7.
15.
BeuersU, SpenglerU, KruisWUrsodeoxycholic acid for treatment of primary sclerosing cholangitis: a placebo-controlled trial.Hepatology1992; 16: 707–14.
16.
ColomboC, SetchellKDR, PoddaMEffects of ursodeoxycholic acid therapy for liver disease associated with cystic fibrosis.J Pediatr1990; 117: 482–9.
17.
ColomboC, CrosignaniA, AssaissoMUrsodeoxycholic acid in cystic fibrosis-associated liver disease: a dose–response study.Hepatology1992; 16: 924–30.
18.
British National Formulary1996; 31: 55.
19.
The Cochrane Collaboration Handbook1994; Section 1.
20.
The Cochrane Database of Systematic Reviews. In: The Cochrane Library. 1996, Issue 3. London: BMJ Publishing Group.
21.
The Cochrane Controlled Trials Register. In: The Cochrane Library.1996, Issue 3. London: BMJ Publishing Group.
22.
Cochrane Collaboration Handbook1994; Section V.
23.
SchulzKF, ChalmersI, HayesRJ, AltmanDG. Empirical evidence of bias. Dimensions of methodological quality associated with estimates of treatment effects in controlled trials.JAMA1995; 273: 408–12.
24.
ColomboC, PoddaM, BattezzatiPMUrsodeoxycholic acid for cystic fibrosis-associated liver disease; final report of a multicenter trial.Hepatology1993; 18: 142A.
25.
ColomboC, BattezzatiPM, SantiniBTreatment with ursodeoxycholic acid for patients with cystic fibrosis and liver disease. In: EscobarH, BaqueroF, SuarezL eds. Clinical ecology of cystic fibrosis.Amsterdam: Elsevier Science Publishers BV1993.
26.
ColomboC, BattezzatiPM, SantiniBUrsodeoxycholic acid (UDCA) for liver disease associated with cystic fibrosis (CF): a double-blind multicenter trial.Proceedings of 18th European Cystic Fibrosis Conference.1993.
27.
Colombo C, Battezzati PM, Podda M, Bettinardi N, Giunta A, and the Italian group for the ‘Study of ursodeoxycholic acid in cystic fibrosis’. Ursodeoxycholic acid for liver disease associated with cystic fibrosis: a double-blind multicenter trial.Hepatology1996; 23: 1484–90.
28.
ColomboC, SetchellKDR, PoddaM, CrosignaniA, AssaissoML, GiuntaA.Ursodeoxycholic acid in cystic fibrosis-associated liver disease: a dose–response study.Proceedings of 17th European Cystic Fibrosis Conference.1991.
29.
BittnerP, SeilerT, OttH, PosseltH-G, MargdorfK, KawinkelM.Therapeutical approach of ursodeoxycholic acid in cystic fibrosis and hepatopathy.Proceedings of 16th European Cystic Fibrosis Conference1989.
30.
NarkewiczMR, SokolRJ, LearJL, WagenerJS, AccursoFJ. Effect of ursodeoxycholic acid (UDCA) therapy for CF liver disease on indirect tests of hepatic function.Proceedings of 8th North American Cystic Fibrosis Conference. Pediatr Pulmonol1994; 310: 342.
31.
MerliM, BertasiS, ServiREffect of a medium dose of ursodeoxycholic acid with or without taurine supplementation on the nutritional status of patients with cystic fibrosis: a randomized, placebo-controlled, crossover trial.J Pediatr Gastroenterol Nutr1994; 19: 198–203.
32.
O'BrienS, FitzgeraldMX, HegartyJE. A controlled trial of ursodeoxycholic acid treatment in cystic fibrosis-related liver disease.Eur J Gastroenterol Hepatol1992; 4: 857–63.