Familial auto-inflammatory Behçet-like syndrome-1 is a rarely reported entity. The clinical manifestations of this condition mimic Behçet's disease in the form of recurrent oral ulcers and gastro-intestinal manifestations. The complete clinical spectrum is yet to be ascertained, as this is a genetic syndrome involving multiple mutations. Here, we report the case of a child with severe malnutrition and failure to thrive in infancy, who turned out to have the said genetic syndrome.
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