We present a young male with recurrent erythema nodosum and recent deep vein thrombosis with scrotal ulcers but no oral ulcers. He was diagnosed as having Behcet's disease (BD) and subsequently responded to immunosuppressants and anticoagulation. This case highlights that up to 2% patients with BD may not have oral ulcers. Timely institution of therapy in our patient resulted in a favorable outcome.
SakaneTTakenoMSuzukiNInabaG. Behcet’s disease. N Engl J Med1999; 341: 1284–1291.
2.
HatemiGYaziciYYaziciH. Behcet's syndrome. Rheum Dis Clin North Am2013; 39: 245–261.
3.
Criteria for diagnosis of Behcet's disease. International Study Group for Behcet’s Disease. Lancet1990; 335: 1078–1080.
4.
International Team for the Revision of the International Criteria for Behcet’s Disease. The International Criteria for Behcet’s Disease (ICBD): a collaborative study of 27 countries on the sensitivity and specificity of the new criteria. J Eur Acad Dermatol Venereol2014; 28: 338–347.
5.
CamargoCMBrotasAMRamos-e-SilvaMCarneiroS. Isomorphic phenomenon of Koebner: facts and controversies. Clin Dermatol2013; 31: 741–749.
6.
BayraktarYBalkanciFBayraktarMCalguneriM. Budd-Chiari syndrome: a common complication of Behcet’s disease. Am J Gastroenterol1997; 92: 858–862.
7.
HatemiGSilmanABangDBodaghiBChamberlainAMGulA. EULAR recommendations for the management of Behcet disease. Ann Rheum Dis2008; 67: 1656–1662.
8.
Tayer-ShifmanOESeyahiENowatzkyJBen-ChetritE. Major vessel thrombosis in Behcet’s disease: the dilemma of anticoagulant therapy - the approach of rheumatologists from different countries. Clin Exp Rheumatol2012; 30: 735–740.