The occurrence of selective IgA deficiency and hypothyroidism with congenital Iymphoedema has never previously been documented, although the association of hypogammaglobulinaemia with congenital Iymphoedema has previously been reported and can result in recurrent respiratory infections. We report a 34 year old woman with congenital Iymphoedema who was found to have symptomatic autoimmune hypothyroidism and asymptomatic selective IgA deficiency.
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