Creutzfeldt-Jakob Disease

Gray JAM. Evidence-based healthcare: the 21st-century agenda. MRC News 1998; 34–37.

Brown P Rau EH Johnson BK Bacote AE Gibbs CJ Jr. Gajdusek DC . New studies on the heat resistance of hamster-adapted scrapie agent: threshold survival after ashing at 600 degrees C suggests an inorganic template of replication. Proc Natl Acad Sci USA 2000; 97:3418–21.

Brown P Preece M Brandel JP Iatrogenic Creutzfeldt-Jakob disease at the millennium. Neurology 2000; 55:1075–81.

Cuill J Chelle PL. La tremblante du mouton est bien inoculable. CR Acad Sci 1938; 206:78–9.

Prusiner SB. Novel proteinaceous infectious particles cause scrapie. Science 1982; 216:136–44.

Hsiao K Baker HF Crow TJ Linkage of a prion protein missense variant to Gerstmann-Str ussier syndrome. Nature 1989; 338:342–5.

Brown P Gibbs CJ Jr. Rodgers-Johnson P Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann Neurol 1994; 35:513–29.

Spencer MD Knight RSG Will RG. First hundred cases of variantCreutzfeldt-Jakob disease: retrospective case note review of early psychiatric and neurological features. BMJ 2002; 324:1479–82.

Lorains JW Henry C Agbamu DA Variant Creutzfeldt-Jakob disease in an elderly patient. Lancet 2001; 357:1339–40.

Macleod MA Stewart GE Zeidler M Will R Knight R. Sensory features of variant Creutzfeldt-Jakob disease. J Neurol 2002; 249:706–11.

Zerr I Pocchiari M Collins S Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease. Neurology 2000; 55:811–15.

Green AJE Thompson EJ Stewart GE Use of 14-3-3 and other brain-specific proteins in the CSF in the diagnosis of variant Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry 2001; 70:744–48.

Schrter A Zerr I Henkel K Tschampa HJ Finkenstaedt M Poser S. Magnetic resonance imaging in the clinical diagnosis of Creutzfeldt Jakob disease. Arch Neurol 2000; 57:1751–57.

Collie DA Sellar RJ Zeidler M Colchester ACF Knight R Will RG. MRI in Creutzfeldt-Jakob disease: imaging features and recommended MRI protocol. Clin Radiol 2001; 56:726–39.

World Health Organization. Report of the WHO consultation on the global surveillance, diagnosis and therapy of human transmissible spongiform encephalopathies. Geneva: WHO; 1998.

World Health Organization, Report of a WHO Consultation on the revision of the variant CJD case definition. Geneva: WHO; 2001.

Hill AF Butterworth RJ Joiner S Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples. Lancet 1999; 353:183–89.

Korth C May BC Cohen FE Prusiner SB. Acridine and phenothiazine derivatives as pharmacotherapeutics for prion disease. Proc Natl Acad Sci U S A 2001; 98:9836–41.

Carrell RW Lomas DA. Conformational disease. Lancet 1997; 350:134–138.