Basic Science Review : The Acid Mucopolysaccharides

Berenson, G.S. , and Serra, M.T. : Polysaccharides in urine from patients with Marfan's syndrome. Fed. Proc. 18: 190, 1959.

Berry, H.K. : Procedures for testing urine specimens dried on filter paper. Clin. Chem. 5: 603, 1959.

Berry, H.K. and Spinanger, J. : A paper spot test useful in study of Hurler's syndrome. J. Lab. Clin. Med. 55: 136, 1960.

Bostrom, H. and Gordell, S. : Uptake of sulfates in mucopolysaccharides esterified with sulfuric acid in the skin of adult rats after intraperitoneal injection of S35 labelled sodium sulfate. Acta Chem. Scand. 7: 216, 1953.

Costar, C.W. and Dorstewitz, E.L. : Identification of acid mucopolysaccharides by paper chromatography. J. Chromatog. 13: 157, 1964.

Di Ferrante, N. and Rich, C. : The determination of acid aminopolysaccharide in urine. J. Lab. Clin. Med. 48: 491, 1956.

Dische, Z. : A new specific color reaction of hexuronic acids. J. Biol. Chem. 167: 189, 1947.

Dorfman, A. : Studies on the biochemistry of connective tissue. Pediatrics 22: 576, 1958.

Dorfman, A. : Metabolism of mucopolysaccharides of connective tissue. Pharmacol. Rev. 7: 1, 1955.

Dorfman, A. and Schiller, S. : Effects of hormones on metabolism of acid mucopolysaccharides of connective tissue. From Recent Progress in Hormone Research, Vol. XIV. New York, Academic Press, 1958, pp. 427-456.

Dorfman, A. and Lorincz, A.E. : Occurrence of urinary acid mucopolysaccharides in the Hurler syndrome. Proc. Nat. Acad. Sci. 43: 443, 1957.

Glaser, L. and Brown, D.H. : The enzymic synthesis in vitro of hyaluronic acid chains. Proc. Natl. Acad. Sci. 41: 253, 1955.

Kaplan, D. and Meyer, K. : The fate of injected mucopolysaccharides. J. Clin. Invest. 41: 743, 1962.

Kerby, G.P. : Excretion of acid mucopolysaccharides in human urine. J. Clin. Invest. 33: 1168, 1954.

King, J.S. : Acid mucopolysaccharides in urine. Chap. 7 in High Molecular Weight Substances in Human Urine. King, J. S. and Boyce, W. H. , Eds. Springfield, Charles C Thomas, 1963, p. 115.

kodieck, E. : Mucopolysaccharides of connective tissue. From Eight Colloquia on Clinical Pathology. M. Welsch , P. Dustin and J. Dagnelie , Eds. Brussels, European Academic Press, 1958, pp. 729-747.

Linker, A. and Terry, K.D. : Urinary acid mucopolysaccharides in normal man and in Hurler's syndrome. Proc. Soc. Exper. Biol. and Med. 113: 743, 1963.

Lorincz, A.E. : Heritable disorders of acid mucopotysaccharide metaabolism in humans and in Snorter dwarf cattle. Ann. N. Y. Acad. Sci. 91: 644,1961.

Mathews, M.B. : The molecular weight of sodium chondroitin sulfate by light scattering. Arch. Biochem. Biophys. 61: 367, 1956.

McKusick, V.A. : Heritable Disorders of Connective Tissue, 2nd Ed. St. Louis, C. V. Mosby Co., 1960, p. 36.

Meyer, K. , Crumbach, M.M. , Linker, A. and Hoffman, P. : Excretion of sulfated mucopolysaccharides in gargoylism (Hurler's syndrome) . Proc. Soc. Exp. Biol. and Med. 97: 275, 1958.

Mittwoch, U. : Inclusions of mucopolysaccharide in lymphocytes of patients with gargoylism. Nature 191: 1315, 1961 .

Pedrini, V. , Lennzi, L. and Zambotti, V. : Isolation and identification of keratosulfate in urine of patients affected by Morquio-Ultrich disease. Proc. Soc. Exp. Biol. and Med. 110: 847, 1962.

Rienitis, K.G. : The electrophoresis of acid mucopolysaccharides on filter paper. Biochem. J. 53: 79, 1953.

Robins, M.M. , Stevens, H.F. and Linker, A. : Morquio's disease: an abnormality of mucopolysaccharide metabolism. J. Pediat. 62: 881, 1963.

Schiller, S. , Mathews, M.B. , Jefferson, H. , Ludoweig, J. and Dorfman, A. : The metabolism of mucopolysaccharides in animals, I. Isolation from skin. J. Biol. Chem. 211: 717, 1954.

Scott, E.J. : The reaction of long-chain quaternary ammonium salts with acid polysaccharides. Chem. and Ind. pp. 168-169, 1955.

Teller, W.M. , Burke, E.C. , Rosevear, J.W. and McKenzie, B.F. : Urinary excretion of acid mucopolysaccharides in normal children and patients with gargoylism. J. Lab. Clin. Meet 59: 95, 1962.

Teller, W.M. , Roseyear, J.W. and Burke, E.C. : Identification of heterozygous carriers of gargoylism. Proc. Soc. Exp. Biol. and Med. 108: 276, 1961.