High Out-Put Congestive Heart Failure as First Manifestation of Osler-Weber-Rendu Disease M. Montejo Baranda,M.D.,F.I.C.a.,M. Perez,M.D.,* J. De Andres,M.D.,* C. De La Hoz,M.D.,J. Merino,M.D.,and C. Aguirre,M.D. Bilbao,Spain
Restricted accessOtherFirst published online September, 1984
High Out-Put Congestive Heart Failure as First Manifestation of Osler-Weber-Rendu Disease M. Montejo Baranda,M.D.,F.I.C.a.,M. Perez,M.D.,* J. De Andres,M.D.,* C. De La Hoz,M.D.,J. Merino,M.D.,and C. Aguirre,M.D. Bilbao,Spain
We present two cases of hemorrhagic he reditary telangiectasia (HHT) or Osler-We ber-Rendu disease which debuted as heart failure. Both had multiple arteriovenous fis tulas, one of them in a rare localization in this disease, a lower extremity. We conclude stressing the importance of thinking of HHT in the presence of obscure heart failure or ar teriovenous fistulas and of looking for inter nal fistulas when faced by a HHT.
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