Double-orifice mitral valve is a rare congenital anomaly. Although it is more frequently associated with other cardiac abnormalities, it may occur as an isolated lesion. There are 2 forms of myocardial noncompaction: isolated and nonisolated myocardial noncompaction. Nonisolated myocardial noncompactions are occasionally reported postnatally in association with congenital heart anomalies such as ventricular septal defect, pulmonic stenosis, and atrial septal defect. To our knowledge, this is the first case presentation reporting a double-orifice mitral valve associated with nonisolated myocardial noncompaction.
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References
1.
Banerjee A, Kohl T, Silverman NH: Echocardiographic evaluation of congenital mitral valve anomalies in children. Am J Cardiol76:1284-1291, 1995.
2.
Yeşilbursa D, Miller A, Nanda NC, et al: Echocardiographic diagnosis of a stenotic double-orifice parachute mitral valve with a single papillary muscle. Echocardiography17:349-352, 2000.
3.
Sasaoka T, Ohguri H, Makita Y, et al: Double-orifice mitral valve in an elderly patient with tetralogy of Fallot. Jpn Heart37:503-507, 1996.
4.
Yamaguchi M, Tachibana H, Hosokawa Y, et al: Ebstein’s anomaly and partial atrioventricular canal associated with double-orifice mitral valve. J Cardiovasc Surg30:790-792, 1989.
5.
Lee CN, Danielson GK, Schaff HV, et al: Surgical treatment of double-orifice mitral valve in atrioventricular canal defects: Experience in 25 patients. J Cardiovasc Surg90:700-705, 1985.
6.
Lee DI, Ha JW, Chung B, et al: Double orifice mitral valve. Clin Cardiol14:429-433, 1984.
7.
Kamei J, Nishino M, Hoshida S: Double-orifice mitral valve associated with noncompaction of left ventricle. Heart85:504, 2001.
8.
Elfenbein B, Palplanus SH: Duplication of the mitral and tricuspid valves. Arch Pathol85:675-680, 1968.
9.
Hartmann B: Zur lehre der verdopplungg des linken atrioventricular ostiums. Arch Kreislauforsch1:286-304, 1937.
10.
Trowitzsch E, Bano-Rodrigo A, Burger BM, et al: Two-dimensional echocardiographic findings in double orifice mitral valve. J Am Coll Cardiol6:383-387, 1985.
11.
Chin TK, Perloff JK, Williams RG, et al: Isolated non-compaction of left ventricular myocardium: A study of eight cases. Circulation82:507-513, 1990.
12.
Ichida F, Tsubata S, Bowles KR, et al: Novel gene mutations in patients with left ventricular noncompaction or Barth syndrome. Circulation103:1256-1263, 2001.
13.
Dusek J, Ostadal B, Duskova M: Postnatal persistence of spongy myocardium with embryonic blood supply. Arch Pathol99:312-317, 1975.
14.
Richardson P, McKenna W, Bristow M, et al: Report of the 1995 World Health Organisation/International Society and Federation of Cardiology Task Force on the definition and classification of cardiomyopathies. Circulation93:841-842, 1996.
15.
Oechslin EN, Jost CHA, Rojas JR, et al: Long-term follow-up of 34 adults with isolated left ventricular noncompaction: A distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol36:493-500, 2000.
