A distinctive case of primary biliary lymphoma occurring in the cystic duct causing extrinsic compression of the porta hepatis in a 48-year-old woman is presented. Imaging studies revealed stricture of the common hepatic duct with a 2.5-cm nonhomogeneous mass at the porta hepatis, mimicking a Klatskin tumor. Exploratory laparotomy revealed a mass in the gallbladder neck with extension into the cystic duct akin to Mirizzi's syndrome. A soft, tan-yellow 1.0-cm mass was removed from the cystic duct, and infiltrating atypical lymphocytic nodules were identified with a final diagnosis of an anaplastic variant of diffuse large B-cell lymphoma.
Get full access to this article
View all access options for this article.
References
1.
DasK., FisherA., WilsonD.Primary non-Hodgkin's lymphoma of the bile ducts mimicking cholangiocarcinoma.Surgery2003; 134: 496–500.
2.
NguyenG.Primary extranodal non-Hodgkin's lymphoma of the extrahepatic bile ducts. Report of a case.Cancer1982; 50: 2218–22.
3.
FergulaD., LuzarB., GadzijevE.Follicular lymphoma of the gallbladder and extrahepatic bile ducts.Virchows Arch2003; 442: 136–40.
4.
EliasonS., GrossoL.Primary biliary malignant lymphoma clinically mimicking cholangiocarcinoma: A case report and review of the literature.Ann Diagn Pathol2001; 5: 25–33.
5.
AndreS., FariasA., BittencourtP.Primary extranodal non-Hodgkin's lymphoma of the extrahepatic bile duct mimmicking [sic] Klatskin tumor.Rev Hosp Clin Fac Med Sao Paulo1996; 51: 192–4.
6.
FreemanM., RoseJ., ForsmarkC., VautheyJ.Mirizzi syndrome: A rare cause of obstructive jaundice.Dig Dis1999; 17: 44–8.
7.
EndoI., NagamineN., NakamuraY.On the Mirizzi syndrome: Benign stenosis of the hepatic duct induced by a stone in the cystic duct or the neck of the gallbladder.Gastroenterol Jpn1979; 14: 155–61.
8.
MoonJ., ChoY., CheonY.Wire-guided intraductal US in the assessment of bile duct strictures with Mirizzi syndrome-like features at ERCP.Gastrointest Endosc2002; 56: 873–9.
9.
AnderS., FariasA., BittencourtP.Primary extranodal non-Hodgkin's lymphoma of the extrahepatic bile duct mimicking Klatskin tumor.Rev Hosp Clin Fac Med Sao Paulo1996; 51: 192–4.
10.
IrieH., HondaH., KanekoK.Primary malignant lymphoma in the porta hepatis: A case report.Abdom Imaging1996; 21: 448–50.
11.
MachadoM., AbdoE., PenteadoS.Lymphoma of the biliary tract: Report of 2 cases.Rev Hosp Clin Fac Med Sao Paulo1994; 49: 64–8.
12.
CorbinaisS., Caulet-MaugendreS., PagenaultM.Primary T-cell lymphoma of the common bile duct.Gastroenterol Clin Biol2000; 24: 843–7.
13.
KosugeT., MakuuchiM., OzakiH.Primary lymphoma of the common bile duct.Hepatogastroenterology1991; 38: 235–8.
