A 57-year-old-man with known tricuspid atresia previously palliated with a Potts shunt had developed progressive heart failure refractory to medical management. He underwent a combined thoracic endovascular stent graft procedure to eliminate the Potts shunt and orthotopic heart transplantation. At 3-month follow-up, right-sided heart function and pulmonary artery pressures as well as pulmonary vascular resistance had normalized, and at 7 months, the patient had returned to normal activity. The surgical management and its principles as well as postoperative follow-up are described.
MairD.D., PugaF.J., DanielsonG.K.The Fontan procedure for tricuspid atresia: early and late results of a 25-year experience with 216 patients. J Am Coll Cardiol.2001; 37: 933–939.
2.
SittiwangkulR., AzakieA., Van ArsdellG.S., WilliamsW.G., McCrindleB.W.Outcomes of tricuspid atresia in the Fontan era. Ann Thorac Surg.2004; 77: 889–894.
3.
PottsW.J., SmithS., GibsonS.Anastomosis of the aorta to a pulmonary artery; certain types in congenital heart disease. J Am Med Assoc.1946; 132: 627–631.
4.
DickM., FylerD.C., NadasA.S.Tricuspid atresia: clinical course in 101 patients. Am J Cardiol.1975; 36: 327–337.
BoshoffD., BudtsW., DaenenW., GewilligM.Transcatheter closure of a Potts’ shunt with subsequent surgical repair of tetralogy of Fallot. Catheter Cardiovasc Interv.2005; 64: 121–123.
7.
OosterhofT., JacobsM., CramerM.J., MulderB.J.Survival into seventh decade after a Potts palliation for tetralogy of Fallot. Congenit Heart Dis.2007; 2: 55–57.
8.
AhmarW., AggarwalA., SkillingtonP., AtkinsonN.Closure of patent Potts shunt with aortic endoluminal stent graft. Cardiovasc Revasc Med.2006; 7: 192–194.
