Abstract
Background:
Hidradenocarcinoma is a malignant tumor of the cutaneous sweat glands. Vulvar lesions are rare, and their prognosis is poor. Recurrence and metastases are common. Surgical excision with ipsilateral lymphadenectomy is recommended.
Case:
A 47-year-old woman presented for consultation after surgical excision with positive margins for eccrine porocarcinoma of the vulva. The resultant right radical vulvectomy suggested a low-grade tumor without lymphovascular space invasion and with negative margins.
Results:
The final diagnosis was invasive hidradenocarcinoma of the vulva. An interval right inguinal lymphadenectomy showed an absence of metastases.
Conclusions:
Hidradenocarcinoma, a rare form of skin cancer affecting the head and neck, should be considered in the differential diagnosis of a vulvar mass. Surgical excision with ipsilateral regional lymphadenectomy can be curative and allow for proper staging. Adjuvant treatment options are limited in number and efficacy.
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