Adnexal Mass with Multiple Peritoneal Nodules in a Young Girl: Report on a Rare Case

Abstract

Abstract

Background:

Gliomatosis peritonei is a rare condition characterized by the presence of implants of mature glial tissue throughout the peritoneum. According to the World Health Organization grading system for immature teratomas, gliomatosis peritonei is assigned to grade 0. Intraoperatively, gliomatosis peritonei is seen as multiple, tiny, well-circumscribed, gray–white peritoneal nodules. Clinicoradiologically, the condition is often misdiagnosed as peritoneal carcinomatosis or peritoneal tuberculosis.

Case:

This article reports on a case of gliomatosis peritonei with an immature teratoma in a 7-year-old girl, who presented with abdominal pain of 1 month's duration. The diagnosis was established after resection of this left adnexal mass along with an omentectomy. Confirmation was established with the help of immunohistochemistry testing.

Results:

The patient was relieved of her abdominal pain and is being followed-up regularly.

Conclusions:

A definitive diagnosis requires histopathologic examination and positive immunohistochemical staining with neural markers. A thorough search for the presence of immature neuroepithelial tissue is imperative in such cases to exclude the possibility of a metastatic immature teratoma.