Multidisciplinary Surgery in a Young Woman with Endometrial Stromal Sarcoma with Inferior Vena Cava and Intracardiac Extension

Abstract

Abstract

Background:

Endometrial stromal sarcoma (ESS) is a rare tumor. Extension into the inferior vena cava (IVC) and heart has been described infrequently.

Case:

A 35-year-old female had low-grade ESS with intracardiac extension. A multidisciplinary team performed laparotomy, hysterectomy, and thoracotomy to obtain access to her intracardiac thrombus and, then, removal of the thrombus in her IVC.

Results:

This successful multidisciplinary team management produced a favorable outcome. This patient is currently being maintained on adjuvant hormonal therapy with 1 mg/day of anastrozole (an aromatase inhibitor to prevent conversion of androgen to estrogen).

Conclusions

: ESS is a rare tumor with intracaval and intracardiac extension. Diagnosis is usually made through histopathology. A multidisciplinary approach is required for optimal management.