Two-Year Survival of Low-Grade Fibromyxoid Sarcoma of the Vulva Managed by Surgical Therapy

Abstract

Abstract

Background:

Low-grade fibromyxoid sarcoma (LGFMS) of the vulva is an exceedingly rare condition. Only two cases of LGFMS arising from the vulva have been reported in the literature.

Case:

A 45-year-old woman presented with a painless, slow-growing left vulvar mass that had evolved for nearly 6 months. She underwent excision of the swelling under a general anesthetic. The final pathologic diagnosis revealed LGFMS of the vulva and a left radical hemivulvectomy was performed.

Results:

After 2 years, this patient remains free of local or metastatic recurrence.

Conclusions:

Although LGFMS of the vulva is uncommon, it should be considered in the differential diagnosis of vulvar lesions. Radical excision is essential to avoid future recurrences.