Müllerian duct anomalies represent a heterogenous group of congenital malformations resulting from abnormal formation or incomplete fusion of Müllerian ducts. Most cases present at puberty or early adulthood with primary amenorrhea or fertility problems although many are asymptomatic and remain undiagnosed. The reported frequency of these anomalies varies, consequent mainly to the inaccuracy of diagnostic methods used and the lack of a uniform classification system. The actual reproductive impact of each anomaly continues to remain ill defined. In addition, radiologic and endoscopic advances appear to have increased the number of unnecessary surgical corrections for these defects. This article attempts to review the reproductive impact of various Müllerian anomalies in a simplified manner. (J GYNECOL SURG 28:127)
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