Ossifying Fibromyxoid Tumor of Soft Parts: An Unusual Pediatric Case

Abstract

We report a case of a 3-year-old female child with an ossifying fibromyxoid tumor of soft parts, the youngest such case to be reported to date. The young age of this patient raises the possibility that the tumor may be congenital arising in developmentally deranged Schwann cells from the neural crest (because of its paraspinous location). This presentation may be unique in this case, or it could be that the usual adult variations represent malignant change in embryologic rests of Schwann cells derived from abnormal neural crest cells.