Surgical Correction of Pseudo-Ainhum in Vohwinkel Syndrome

Abstract

Vohwinkel syndrome or hereditary mutilating keratodermatitis is a rare condition producing palmo-plantar hyperkeratosis and constricting rings of the fingers and toes which can progress to compromise neurovascular function and mobility. Medical treatment with oral retinol derivatives is recommended when its use is not contra-indicated. This paper describes surgical correction of the constricting rings on both hands in a 33-year-old woman affected by this condition.